Sacrococcygeal teratoma (SCT) is a rare congenital disease and prognostic factors are not entirely established. We report two cases of fetal SCT with different clinical courses. Case 1 was cystic, slow growing tumor with mild vascularity. The tumor was removed one week after delivery at 35 weeks, and it has been no recurrence at 1.5 year follow up. Case 2 was solid, rapid growing tumor with rich vascularity. Cesarean section was performed due to severe fetal hydrops and mother's Mirror syndrome at 27 weeks. The tumor had been ruptured and was removed soon after delivery to control bleeding, but the baby died on the next day. Our cases suggested that solid component and rich vascularity might correlate with poor prognosis.
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